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What is your approach to the treatment of gamma heavy chain disease (Franklin's disease)?
How do you distinguish this entity from other plasma cell disorders (eg. MGUS, MM, etc.)?
Review of literature suggests that most of these patients have been treated with CVP or alkylators plus corticosteroids with poor results. Is there experience with newer agents or regimens utilized for myeloma?
Answer from: Medical Oncologist at Academic Institution
This is such a rare entity and it has been treated with so many different regimens.It is hard to diagnose and I have seen very a handful of cases over the years. The presentation can be variable and include lymphadenopathy, anemia, splenomegaly, skin involvement, thrombocytopenia, and rarely hepatom...
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