What is your approach to treatment for MDA5 dermatomyositis patients with rapidly progressive ILD?
Cyclophosphamide/tacrolimus and Rituximab have been used in conjunction with steroids in case series.
Answer from: at Academic Institution
Rapidly progressive ILD is a temporal term, describing rapidly declining lung function within weeks (usually defined as 3 months). Therefore, we commonly use this term when the patient is already hospitalized with respiratory failure. The majority of the data stem from Japan and China, where they en...