What is the appropriate dose/fractionation when treating a dermatofibrosarcoma protuberans of the spine following debulking surgery in a patient with a good performance status?
In this patient dermatofibrosarcoma protuberans of the thoracic spine, which originally caused a cord compression and has since been debulked, gross residual disease remains.
Answer from: Radiation Oncologist at Academic Institution
Certainly, a challenging circumstance. With DFSP, pathology review is critical to evaluate for transformation to more aggressive variants with higher malignant potential. Clinically, DFSP is usually present for decades and extremely slow growing. Sudden changes in growth rate are concerning for tran...